Familial mediterranean fever

From WikiMD.org
Jump to navigation Jump to search

Familial Mediterranean Fever (pronunciation: /fəˈmɪliəl ˌmɛdɪtəˈriːən ˈfiːvər/), often abbreviated as FMF, is a hereditary inflammatory disorder. FMF is an autosomal recessive disease, which means it occurs when an individual inherits two copies of an abnormal gene for the same trait.

Etymology

The term "Familial" refers to the genetic nature of the disease, "Mediterranean" refers to the geographic distribution of the disease, and "Fever" refers to the recurrent fevers that are a key symptom of the disease.

Symptoms

The primary symptoms of FMF are recurrent episodes of fever, accompanied by pain in the abdomen, chest, or joints. These episodes are often accompanied by a rash or headache.

Causes

FMF is caused by mutations in the MEFV gene. This gene provides instructions for making a protein called pyrin, which plays a role in the immune system.

Diagnosis

Diagnosis of FMF is based on clinical findings (symptoms and physical examination) and can be confirmed by genetic testing.

Treatment

Treatment for FMF primarily involves managing symptoms. This can include the use of medications such as colchicine to prevent or reduce the frequency of fever episodes.

Prognosis

With proper treatment, individuals with FMF can lead normal lives. However, without treatment, FMF can lead to complications such as amyloidosis, which can be life-threatening.

See also

External links

Esculaap.svg

This WikiMD article is a stub. You can help make it a full article.


Languages: - East Asian 中文, 日本, 한국어, South Asian हिन्दी, Urdu, বাংলা, తెలుగు, தமிழ், ಕನ್ನಡ,
Southeast Asian Indonesian, Vietnamese, Thai, မြန်မာဘာသာ, European español, Deutsch, français, русский, português do Brasil, Italian, polski