Waldmann disease
Waldmann disease (pronounced: wald-man di-zeez), also known as Primary Intestinal Lymphangiectasia (PIL), is a rare disorder characterized by the enlargement and malfunctioning of the lymphatic vessels within the small intestine. The disease was first described by Dr. Thomas A. Waldmann in 1961.
Etymology
The disease is named after Dr. Thomas A. Waldmann, an American immunologist who first described the condition in 1961. The term 'lymphangiectasia' is derived from the Greek words 'lymph' meaning 'clear fluid', 'angeion' meaning 'vessel', and 'ektasis' meaning 'dilation'.
Symptoms
The symptoms of Waldmann disease include protein-losing enteropathy, edema (swelling), malabsorption, and malnutrition. These symptoms are due to the leakage of lymphatic fluid into the intestines, leading to a loss of proteins and other vital nutrients.
Diagnosis
Diagnosis of Waldmann disease is typically made through a combination of clinical findings, laboratory tests, and imaging studies. Endoscopy and biopsy of the small intestine are often used to confirm the diagnosis.
Treatment
Treatment for Waldmann disease is primarily focused on managing the symptoms and preventing complications. This may include a low-fat diet, supplementation with medium-chain triglycerides, and in some cases, surgical intervention.
Prognosis
The prognosis for individuals with Waldmann disease varies. Some individuals may experience a mild form of the disease and live a normal lifespan, while others may experience severe symptoms and complications.
See also
External links
- Medical encyclopedia article on Waldmann disease
- Wikipedia's article - Waldmann disease
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