Hydranencephaly

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Hydranencephaly

Hydranencephaly (pronounced hi-dran-en-sef-uh-lee) is a rare neurological disorder that affects the brain of an individual.

Etymology

The term "Hydranencephaly" is derived from three Greek words: "hydro" meaning water, "an" meaning without, and "encephalon" meaning brain. Thus, it literally translates to "water instead of brain".

Definition

Hydranencephaly is a condition in which the brain's cerebral hemispheres are absent to varying degrees and the remaining cranial cavity is filled with cerebrospinal fluid.

Symptoms

The symptoms of hydranencephaly may include microcephaly (abnormally small head), spastic quadriparesis (paralysis of all four limbs), and intellectual disability.

Causes

The exact cause of hydranencephaly is unknown. However, it is believed to occur due to vascular insufficiency during the prenatal period, leading to necrosis of the cerebral tissue.

Diagnosis

Diagnosis of hydranencephaly can be made through ultrasound during pregnancy or after birth through MRI or CT scan.

Treatment

There is no cure for hydranencephaly. Treatment is symptomatic and supportive, focusing on managing the symptoms and improving the quality of life of the individual.

Prognosis

The prognosis for individuals with hydranencephaly is poor, with most individuals not surviving past infancy. However, with appropriate supportive care, some individuals may live into childhood or adolescence.

Related Terms

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