Apolipoprotein B deficiency

From WikiMD.org
Jump to navigation Jump to search

Apolipoprotein B deficiency

Apolipoprotein B deficiency (pronunciation: a-po-li-po-pro-tein B de-fi-cien-cy) is a rare genetic disorder characterized by low levels of Apolipoprotein B (ApoB) in the body.

Etymology

The term "Apolipoprotein B deficiency" is derived from the Greek words "apo" (away from), "lipos" (fat), "protein", and "deficiency". It refers to the lack of Apolipoprotein B, a protein that plays a crucial role in fat metabolism.

Definition

Apolipoprotein B deficiency is a condition that impairs the body's ability to absorb and transport fats and cholesterol. This deficiency is caused by mutations in the APOB gene, which provides instructions for making Apolipoprotein B.

Symptoms

The symptoms of Apolipoprotein B deficiency include malabsorption, failure to thrive, and neurological symptoms such as ataxia and retinitis pigmentosa.

Diagnosis

Diagnosis of Apolipoprotein B deficiency is based on clinical symptoms, blood tests showing low levels of Apolipoprotein B, and genetic testing confirming mutations in the APOB gene.

Treatment

Treatment for Apolipoprotein B deficiency involves dietary modifications to manage malabsorption and nutritional supplementation to address deficiencies.

Related Terms

External links

Esculaap.svg

This WikiMD article is a stub. You can help make it a full article.


Languages: - East Asian 中文, 日本, 한국어, South Asian हिन्दी, Urdu, বাংলা, తెలుగు, தமிழ், ಕನ್ನಡ,
Southeast Asian Indonesian, Vietnamese, Thai, မြန်မာဘာသာ, European español, Deutsch, français, русский, português do Brasil, Italian, polski