Mitochondrial myopathy

From WikiMD.org
Jump to navigation Jump to search

Mitochondrial Myopathy

Mitochondrial myopathy (/maɪtoʊkɒndriːəl maɪˈɒpəθi/) is a group of neuromuscular diseases caused by damage to the mitochondria—small, energy-producing structures that serve as the cells' "power plants."

Etymology

The term "mitochondrial myopathy" is derived from the Greek words "mitos" (thread) and "chondrion" (granule) for mitochondria, and "myo" (muscle) and "pathos" (suffering) for myopathy.

Definition

Mitochondrial myopathies are a type of myopathy associated with mitochondrial disease. They are the result of genetic mutations, often inherited, that lead to poorly functioning or non-functioning mitochondria.

Symptoms

Symptoms of mitochondrial myopathy can include muscle weakness, exercise intolerance, heart failure or rhythm disturbances, dementia, movement disorders, stroke-like episodes, deafness, blindness, droopy eyelids, limited mobility of the eyes, vomiting, and seizures.

Diagnosis

Diagnosis of mitochondrial myopathy often involves a muscle biopsy, which reveals ragged red fibers when stained and viewed under a microscope. Genetic testing can also be used to identify the specific mutation causing the disease.

Treatment

There is currently no cure for mitochondrial myopathies. Treatment is symptomatic and supportive, and may include physical therapy, respiratory therapy, and the use of mobility aids.

Related Terms

External links

Esculaap.svg

This WikiMD article is a stub. You can help make it a full article.


Languages: - East Asian 中文, 日本, 한국어, South Asian हिन्दी, Urdu, বাংলা, తెలుగు, தமிழ், ಕನ್ನಡ,
Southeast Asian Indonesian, Vietnamese, Thai, မြန်မာဘာသာ, European español, Deutsch, français, русский, português do Brasil, Italian, polski