Diktyoma: Difference between revisions
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{{Infobox medical condition | |||
| name = Diktyoma | |||
| image = [[File:Medulloepithelioma_Histology.jpg|250px]] | |||
| caption = Histological image of a medulloepithelioma, also known as diktyoma | |||
| field = [[Ophthalmology]] | |||
| synonyms = [[Medulloepithelioma]] | |||
| symptoms = [[Vision loss]], [[eye pain]], [[proptosis]] | |||
| complications = [[Glaucoma]], [[retinal detachment]] | |||
| onset = Typically in [[childhood]] | |||
| duration = [[Chronic (medicine)|Chronic]] | |||
| types = [[Teratoid]], [[non-teratoid]] | |||
| causes = [[Congenital]] | |||
| risks = [[Genetic predisposition]] | |||
| diagnosis = [[Ophthalmic examination]], [[imaging studies]], [[biopsy]] | |||
| differential = [[Retinoblastoma]], [[Coats' disease]] | |||
| prevention = None known | |||
| treatment = [[Surgical resection]], [[radiation therapy]], [[chemotherapy]] | |||
| medication = None specific | |||
| prognosis = Variable, depends on extent and treatment | |||
| frequency = Rare | |||
}} | |||
{{Short description|A rare, primitive neuroectodermal tumor of the eye}} | {{Short description|A rare, primitive neuroectodermal tumor of the eye}} | ||
Diktyoma, also known as medulloepithelioma, is a rare, primitive neuroectodermal tumor that primarily affects the [[eye]]. It is most commonly found in children and is characterized by its origin from the non-pigmented ciliary epithelium of the [[ciliary body]]. | Diktyoma, also known as medulloepithelioma, is a rare, primitive neuroectodermal tumor that primarily affects the [[eye]]. It is most commonly found in children and is characterized by its origin from the non-pigmented ciliary epithelium of the [[ciliary body]]. | ||
==Pathophysiology== | ==Pathophysiology== | ||
Diktyomas are believed to arise from the primitive medullary epithelium, which is a remnant of the embryonic neural tube. These tumors are composed of neuroepithelial cells that can differentiate into a variety of cell types, including neuronal, glial, and epithelial cells. The histological appearance of diktyoma is often described as resembling the embryonic neural tube, with rosettes and tubular structures. | Diktyomas are believed to arise from the primitive medullary epithelium, which is a remnant of the embryonic neural tube. These tumors are composed of neuroepithelial cells that can differentiate into a variety of cell types, including neuronal, glial, and epithelial cells. The histological appearance of diktyoma is often described as resembling the embryonic neural tube, with rosettes and tubular structures. | ||
==Clinical Presentation== | ==Clinical Presentation== | ||
Patients with diktyoma typically present with symptoms related to the [[eye]], such as decreased vision, eye pain, or visible mass in the eye. In some cases, the tumor may cause secondary [[glaucoma]] or [[retinal detachment]]. | Patients with diktyoma typically present with symptoms related to the [[eye]], such as decreased vision, eye pain, or visible mass in the eye. In some cases, the tumor may cause secondary [[glaucoma]] or [[retinal detachment]]. | ||
==Diagnosis== | ==Diagnosis== | ||
The diagnosis of diktyoma is primarily based on clinical examination and imaging studies. [[Ultrasound]] and [[magnetic resonance imaging]] (MRI) are commonly used to assess the extent of the tumor. Definitive diagnosis is made through histopathological examination of the tumor tissue, which reveals the characteristic features of medulloepithelioma. | The diagnosis of diktyoma is primarily based on clinical examination and imaging studies. [[Ultrasound]] and [[magnetic resonance imaging]] (MRI) are commonly used to assess the extent of the tumor. Definitive diagnosis is made through histopathological examination of the tumor tissue, which reveals the characteristic features of medulloepithelioma. | ||
==Treatment== | ==Treatment== | ||
The treatment of diktyoma depends on the size and location of the tumor, as well as the presence of any complications. Surgical removal of the tumor is the primary treatment modality. In some cases, [[enucleation]] of the affected eye may be necessary. Adjuvant therapies, such as [[radiation therapy]] or [[chemotherapy]], may be considered in cases where complete surgical resection is not possible. | The treatment of diktyoma depends on the size and location of the tumor, as well as the presence of any complications. Surgical removal of the tumor is the primary treatment modality. In some cases, [[enucleation]] of the affected eye may be necessary. Adjuvant therapies, such as [[radiation therapy]] or [[chemotherapy]], may be considered in cases where complete surgical resection is not possible. | ||
==Prognosis== | ==Prognosis== | ||
The prognosis for patients with diktyoma varies depending on the extent of the disease and the success of treatment. Early detection and complete surgical removal of the tumor are associated with a better prognosis. However, the potential for local recurrence and metastasis exists, particularly in cases where the tumor is not completely resected. | The prognosis for patients with diktyoma varies depending on the extent of the disease and the success of treatment. Early detection and complete surgical removal of the tumor are associated with a better prognosis. However, the potential for local recurrence and metastasis exists, particularly in cases where the tumor is not completely resected. | ||
==See also== | |||
== | |||
* [[Retinoblastoma]] | * [[Retinoblastoma]] | ||
* [[Neuroectodermal tumor]] | * [[Neuroectodermal tumor]] | ||
* [[Ciliary body]] | * [[Ciliary body]] | ||
[[Category:Ophthalmology]] | [[Category:Ophthalmology]] | ||
[[Category:Neuroectodermal tumors]] | [[Category:Neuroectodermal tumors]] | ||
Latest revision as of 18:38, 5 April 2025
Editor-In-Chief: Prab R Tumpati, MD
Obesity, Sleep & Internal medicine
Founder, WikiMD Wellnesspedia &
W8MD medical weight loss NYC and sleep center NYC
| Diktyoma | |
|---|---|
| |
| Synonyms | Medulloepithelioma |
| Pronounce | N/A |
| Specialty | N/A |
| Symptoms | Vision loss, eye pain, proptosis |
| Complications | Glaucoma, retinal detachment |
| Onset | Typically in childhood |
| Duration | Chronic |
| Types | Teratoid, non-teratoid |
| Causes | Congenital |
| Risks | Genetic predisposition |
| Diagnosis | Ophthalmic examination, imaging studies, biopsy |
| Differential diagnosis | Retinoblastoma, Coats' disease |
| Prevention | None known |
| Treatment | Surgical resection, radiation therapy, chemotherapy |
| Medication | None specific |
| Prognosis | Variable, depends on extent and treatment |
| Frequency | Rare |
| Deaths | N/A |
A rare, primitive neuroectodermal tumor of the eye
Diktyoma, also known as medulloepithelioma, is a rare, primitive neuroectodermal tumor that primarily affects the eye. It is most commonly found in children and is characterized by its origin from the non-pigmented ciliary epithelium of the ciliary body.
Pathophysiology[edit]
Diktyomas are believed to arise from the primitive medullary epithelium, which is a remnant of the embryonic neural tube. These tumors are composed of neuroepithelial cells that can differentiate into a variety of cell types, including neuronal, glial, and epithelial cells. The histological appearance of diktyoma is often described as resembling the embryonic neural tube, with rosettes and tubular structures.
Clinical Presentation[edit]
Patients with diktyoma typically present with symptoms related to the eye, such as decreased vision, eye pain, or visible mass in the eye. In some cases, the tumor may cause secondary glaucoma or retinal detachment.
Diagnosis[edit]
The diagnosis of diktyoma is primarily based on clinical examination and imaging studies. Ultrasound and magnetic resonance imaging (MRI) are commonly used to assess the extent of the tumor. Definitive diagnosis is made through histopathological examination of the tumor tissue, which reveals the characteristic features of medulloepithelioma.
Treatment[edit]
The treatment of diktyoma depends on the size and location of the tumor, as well as the presence of any complications. Surgical removal of the tumor is the primary treatment modality. In some cases, enucleation of the affected eye may be necessary. Adjuvant therapies, such as radiation therapy or chemotherapy, may be considered in cases where complete surgical resection is not possible.
Prognosis[edit]
The prognosis for patients with diktyoma varies depending on the extent of the disease and the success of treatment. Early detection and complete surgical removal of the tumor are associated with a better prognosis. However, the potential for local recurrence and metastasis exists, particularly in cases where the tumor is not completely resected.
