Double outlet right ventricle

Double outlet right ventricle
Synonyms	DORV
Pronounce	N/A
Specialty	N/A
Symptoms	Cyanosis, shortness of breath, heart murmur
Complications	Heart failure, pulmonary hypertension
Onset	Congenital
Duration	Chronic
Types	Tetralogy of Fallot-type, Transposition of the great arteries-type
Causes	Genetic mutations, environmental factors
Risks	Family history, maternal diabetes, maternal alcohol use
Diagnosis	Echocardiogram, cardiac MRI, chest X-ray
Differential diagnosis	Tetralogy of Fallot, ventricular septal defect, transposition of the great arteries
Prevention	Prenatal care, genetic counseling
Treatment	Surgical repair, medications
Medication	Diuretics, ACE inhibitors, beta blockers
Prognosis	Variable, depends on surgical outcome
Frequency	Rare
Deaths	Depends on severity and treatment

Double Outlet Right Ventricle (DORV) is a congenital heart defect where both the pulmonary artery and the aorta arise from the right ventricle. This condition is often associated with a ventricular septal defect (VSD), which allows blood to mix between the two ventricles.

Overview

In a normal heart, the right ventricle pumps blood to the lungs through the pulmonary artery, while the left ventricle pumps blood to the rest of the body through the aorta. In a heart with DORV, both of these major arteries come out of the right ventricle. This means that oxygen-rich blood from the lungs and oxygen-poor blood from the body are mixed together before being pumped out to the body.

Symptoms

Symptoms of DORV can vary greatly depending on the size and location of the VSD and the degree of pulmonary stenosis. Common symptoms include cyanosis (bluish color of the skin, lips, and nail beds), shortness of breath, rapid breathing, poor feeding, and poor weight gain.

Diagnosis

DORV is typically diagnosed through a combination of echocardiography, cardiac catheterization, and cardiac MRI. These tests can help determine the structure of the heart and the flow of blood through the heart.

Treatment

Treatment for DORV typically involves surgery to redirect the flow of blood through the heart. The specific type of surgery will depend on the individual's specific heart anatomy. In some cases, multiple surgeries may be needed.

Prognosis

The prognosis for individuals with DORV can vary greatly depending on the severity of the condition and the individual's overall health. With appropriate treatment, many individuals with DORV can lead healthy, productive lives.

See Also

• Congenital heart defect
• Pulmonary artery
• Aorta
• Right ventricle
• Ventricular septal defect
• Pulmonary stenosis
• Cyanosis
• Echocardiography
• Cardiac catheterization
• Cardiac MRI