Primary lymphedema
Primary Lymphedema
Primary lymphedema (pronunciation: pri·ma·ry | \ ˈprī-ˌmer-ē \ lymphedema | \ lim-fə-ˈdē-mə \) is a rare, inherited condition characterized by swelling (edema) of certain parts of the body caused by abnormalities in the lymphatic system.
Etymology
The term 'Primary lymphedema' is derived from the Greek words 'prôtos' meaning 'first' and 'lymphedema' which is a combination of 'lymph' and 'edema'. 'Lymph' comes from the Latin 'lympha' meaning 'water', and 'edema' from the Greek 'oidēma' meaning 'swelling'.
Definition
Primary lymphedema is a type of lymphedema that is present at birth (congenital) or develops later in life (late-onset), without any apparent cause. It is caused by a malformation or malfunction of the lymphatic system, which is responsible for draining excess fluid from body tissues.
Symptoms
The main symptom of primary lymphedema is persistent swelling, usually in the arms or legs, caused by a buildup of lymph fluid. Other symptoms may include a feeling of heaviness, discomfort, repeated skin infections, and thickening and hardening of the skin in the affected area.
Types
There are three types of primary lymphedema:
- Congenital lymphedema: This type is present at birth and is caused by problems with the development of the lymphatic system in the womb.
- Lymphedema praecox: This type develops during puberty, usually between the ages of 1 and 35.
- Lymphedema tarda: This type develops later in life, usually after the age of 35.
Treatment
Treatment for primary lymphedema focuses on managing the symptoms and includes compression therapy, manual lymphatic drainage, and exercise therapy. In some cases, surgery may be recommended.
See Also
External links
- Medical encyclopedia article on Primary lymphedema
- Wikipedia's article - Primary lymphedema
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