Endolymphatic sac tumor

Endolymphatic Sac Tumor is a rare, slow-growing tumor that originates in the endolymphatic sac, a part of the inner ear. These tumors are associated with Von Hippel-Lindau disease, a genetic condition that causes tumors and cysts to grow in the body.

Symptoms

The symptoms of an endolymphatic sac tumor can vary, but often include:

• Hearing loss
• Tinnitus (ringing in the ears)
• Vertigo (a sense of spinning)
• Facial nerve paralysis

Diagnosis

Diagnosis of an endolymphatic sac tumor typically involves a combination of medical history, physical examination, and imaging tests such as MRI or CT scan.

Treatment

Treatment options for endolymphatic sac tumors include:

• Surgery to remove the tumor
• Radiation therapy
• Chemotherapy

Prognosis

The prognosis for individuals with an endolymphatic sac tumor varies depending on the size and location of the tumor, as well as the individual's overall health.

See Also

• Von Hippel-Lindau disease
• Inner ear
• Hearing loss
• Tinnitus
• Vertigo
• Facial nerve paralysis
• MRI
• CT scan
• Surgery
• Radiation therapy
• Chemotherapy

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  Post contrast T1 weighted MRI demonstrates intense enhancement of both the eye and the endolymphatic sac tumor.
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  CT through the petrous ridge showing endolymphatic sac tumor in Von Hippel-Lindau disease.
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  Ear Endolymphatic Sac Tumor H and E Low power.
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  Ear Endolymphatic Sac Tumor H & E High power.