Giant platelet syndrome

From WikiMD.org
Jump to navigation Jump to search

Giant Platelet Syndrome

Giant Platelet Syndrome (pronunciation: /ˈdʒaɪənt ˈpleɪtlɪt ˈsɪndroʊm/), also known as Bernard-Soulier Syndrome, is a rare inherited bleeding disorder characterized by the presence of unusually large platelets in the blood.

Etymology

The term "Giant Platelet Syndrome" is derived from the distinctive feature of the disorder, which is the presence of abnormally large platelets. The syndrome is also named after the French hematologists Jean Bernard and Jean Pierre Soulier who first described the condition in 1948.

Definition

Giant Platelet Syndrome is a disorder that affects the blood clotting process. It is characterized by unusually large platelets, a low number of platelets, and prolonged bleeding time. This condition is caused by mutations in the GP1BA, GP1BB, or GP9 genes.

Symptoms

The symptoms of Giant Platelet Syndrome can vary, but they often include easy bruising, prolonged bleeding, nosebleeds, and bleeding gums. In severe cases, individuals may experience bleeding into the joints or internal bleeding.

Diagnosis

Diagnosis of Giant Platelet Syndrome typically involves blood tests to measure platelet count and size, as well as tests to assess the function of the platelets. Genetic testing may also be performed to identify mutations in the GP1BA, GP1BB, or GP9 genes.

Treatment

Treatment for Giant Platelet Syndrome is typically focused on managing symptoms and preventing bleeding episodes. This may involve the use of medications to increase platelet count, as well as procedures to stop or prevent bleeding.

Related Terms

External links

Esculaap.svg

This WikiMD article is a stub. You can help make it a full article.


Languages: - East Asian 中文, 日本, 한국어, South Asian हिन्दी, Urdu, বাংলা, తెలుగు, தமிழ், ಕನ್ನಡ,
Southeast Asian Indonesian, Vietnamese, Thai, မြန်မာဘာသာ, European español, Deutsch, français, русский, português do Brasil, Italian, polski