Blue diaper syndrome

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Blue Diaper Syndrome

Blue Diaper Syndrome (pronounced: bloo dai-per sin-drohm) is a rare metabolic disorder that is characterized by the abnormal presence of a blue or greenish color in the urine or feces. The condition is also known as Drummond's Syndrome or Tryptophan Malabsorption Syndrome.

Etymology

The term "Blue Diaper Syndrome" is derived from the distinctive blue or greenish color that appears in the urine or feces of affected individuals, often noticeable in their diapers. The syndrome was first described by Drummond and Matthew in 1964, hence the alternative name, Drummond's Syndrome.

Symptoms

The primary symptom of Blue Diaper Syndrome is the abnormal coloration of urine and feces. Other symptoms may include intellectual disability, hypercalcemia (excessive calcium in the blood), and nephrocalcinosis (calcium deposits in the kidneys).

Causes

Blue Diaper Syndrome is caused by a defect in the body's ability to absorb the essential amino acid tryptophan. This results in an excessive amount of tryptophan being excreted in the urine, which reacts with air to produce the characteristic blue or greenish color.

Diagnosis

Diagnosis of Blue Diaper Syndrome is typically made through a combination of clinical examination and laboratory testing, including urine tests to detect the presence of excessive tryptophan.

Treatment

Treatment for Blue Diaper Syndrome primarily involves dietary management to ensure adequate intake of tryptophan. In some cases, medication may be prescribed to manage associated symptoms such as hypercalcemia and nephrocalcinosis.

See Also

External links

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