Lymphangiomatosis: Difference between revisions
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'''Lymphangiomatosis''' is a rare, non-malignant disease characterized by the abnormal growth of lymph vessels. It can affect multiple organs in the body, including the lungs, liver, spleen, and bones. The disease is most commonly diagnosed in children and young adults, but it can occur at any age. | {{SI}} {{Infobox medical condition | ||
| name = Lymphangiomatosis | |||
| image = [[File:Lung_biopsy_showing_infiltration_of_lymphatic_tissue.png|250px]] | |||
| caption = Lung biopsy showing infiltration of lymphatic tissue | |||
| field = [[Vascular medicine]] | |||
| synonyms = | |||
| symptoms = [[Dyspnea]], [[cough]], [[chest pain]], [[pleural effusion]] | |||
| complications = [[Respiratory failure]], [[chylothorax]] | |||
| onset = | |||
| duration = | |||
| types = | |||
| causes = Abnormal proliferation of [[lymphatic vessels]] | |||
| risks = | |||
| diagnosis = [[Imaging studies]], [[biopsy]] | |||
| differential = [[Lymphangioleiomyomatosis]], [[sarcoidosis]], [[tuberculosis]] | |||
| prevention = | |||
| treatment = [[Symptomatic treatment]], [[surgery]], [[medications]] | |||
| medication = | |||
| prognosis = Variable, depends on extent and location | |||
| frequency = Rare | |||
| deaths = | |||
}} | |||
[[Category:Vascular diseases]] | |||
[[Category:Rare diseases]]'''Lymphangiomatosis''' is a rare, non-malignant disease characterized by the abnormal growth of lymph vessels. It can affect multiple organs in the body, including the lungs, liver, spleen, and bones. The disease is most commonly diagnosed in children and young adults, but it can occur at any age. | |||
== Symptoms == | == Symptoms == | ||
The symptoms of lymphangiomatosis vary depending on the organs affected. Common symptoms include: | The symptoms of lymphangiomatosis vary depending on the organs affected. Common symptoms include: | ||
* [[Breathing difficulties]] | * [[Breathing difficulties]] | ||
* [[Coughing]] | * [[Coughing]] | ||
| Line 11: | Line 32: | ||
* [[Fatigue]] | * [[Fatigue]] | ||
* [[Weight loss]] | * [[Weight loss]] | ||
== Causes == | == Causes == | ||
The exact cause of lymphangiomatosis is unknown. It is thought to be a result of a developmental error in the formation of the [[lymphatic system]]. | The exact cause of lymphangiomatosis is unknown. It is thought to be a result of a developmental error in the formation of the [[lymphatic system]]. | ||
== Diagnosis == | == Diagnosis == | ||
Diagnosis of lymphangiomatosis is often challenging due to the rarity of the disease and the variability of symptoms. It typically involves a combination of [[medical history]], physical examination, imaging studies such as [[CT scan]] or [[MRI]], and sometimes tissue biopsy. | Diagnosis of lymphangiomatosis is often challenging due to the rarity of the disease and the variability of symptoms. It typically involves a combination of [[medical history]], physical examination, imaging studies such as [[CT scan]] or [[MRI]], and sometimes tissue biopsy. | ||
== Treatment == | == Treatment == | ||
There is currently no cure for lymphangiomatosis. Treatment is aimed at managing symptoms and improving quality of life. This may include: | There is currently no cure for lymphangiomatosis. Treatment is aimed at managing symptoms and improving quality of life. This may include: | ||
* [[Pain management]] | * [[Pain management]] | ||
* [[Physical therapy]] | * [[Physical therapy]] | ||
| Line 26: | Line 43: | ||
* [[Radiation therapy]] | * [[Radiation therapy]] | ||
* [[Chemotherapy]] | * [[Chemotherapy]] | ||
== Prognosis == | == Prognosis == | ||
The prognosis for individuals with lymphangiomatosis varies widely. Some individuals may live a normal lifespan with few symptoms, while others may experience severe complications and reduced life expectancy. | The prognosis for individuals with lymphangiomatosis varies widely. Some individuals may live a normal lifespan with few symptoms, while others may experience severe complications and reduced life expectancy. | ||
== See also == | == See also == | ||
* [[Lymphatic system]] | * [[Lymphatic system]] | ||
* [[Lymphatic disease]] | * [[Lymphatic disease]] | ||
* [[Lymphangioma]] | * [[Lymphangioma]] | ||
[[Category:Rare diseases]] | [[Category:Rare diseases]] | ||
[[Category:Lymphatic system disorders]] | [[Category:Lymphatic system disorders]] | ||
{{stub}} | {{stub}} | ||
Latest revision as of 03:12, 6 April 2025
Editor-In-Chief: Prab R Tumpati, MD
Obesity, Sleep & Internal medicine
Founder, WikiMD Wellnesspedia &
W8MD medical weight loss NYC and sleep center NYC
| Lymphangiomatosis | |
|---|---|
| |
| Synonyms | |
| Pronounce | N/A |
| Specialty | N/A |
| Symptoms | Dyspnea, cough, chest pain, pleural effusion |
| Complications | Respiratory failure, chylothorax |
| Onset | |
| Duration | |
| Types | |
| Causes | Abnormal proliferation of lymphatic vessels |
| Risks | |
| Diagnosis | Imaging studies, biopsy |
| Differential diagnosis | Lymphangioleiomyomatosis, sarcoidosis, tuberculosis |
| Prevention | |
| Treatment | Symptomatic treatment, surgery, medications |
| Medication | |
| Prognosis | Variable, depends on extent and location |
| Frequency | Rare |
| Deaths | |
Lymphangiomatosis is a rare, non-malignant disease characterized by the abnormal growth of lymph vessels. It can affect multiple organs in the body, including the lungs, liver, spleen, and bones. The disease is most commonly diagnosed in children and young adults, but it can occur at any age.
Symptoms[edit]
The symptoms of lymphangiomatosis vary depending on the organs affected. Common symptoms include:
Causes[edit]
The exact cause of lymphangiomatosis is unknown. It is thought to be a result of a developmental error in the formation of the lymphatic system.
Diagnosis[edit]
Diagnosis of lymphangiomatosis is often challenging due to the rarity of the disease and the variability of symptoms. It typically involves a combination of medical history, physical examination, imaging studies such as CT scan or MRI, and sometimes tissue biopsy.
Treatment[edit]
There is currently no cure for lymphangiomatosis. Treatment is aimed at managing symptoms and improving quality of life. This may include:
- Pain management
- Physical therapy
- Surgery to remove or reduce the size of the abnormal lymph vessels
- Radiation therapy
- Chemotherapy
Prognosis[edit]
The prognosis for individuals with lymphangiomatosis varies widely. Some individuals may live a normal lifespan with few symptoms, while others may experience severe complications and reduced life expectancy.
