Hydroa vacciniforme: Difference between revisions
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{{SI}} | |||
{{Infobox medical condition | |||
| name = Hydroa vacciniforme | |||
| image = [[File:An_introduction_to_dermatology_(1905)_Hydroa_vacciniforme.jpg|250px]] | |||
| caption = Hydroa vacciniforme lesions on the skin | |||
| synonyms = | |||
| pronounce = | |||
| specialty = [[Dermatology]] | |||
| symptoms = [[Vesicular]] skin lesions, [[scarring]], [[photosensitivity]] | |||
| onset = Childhood | |||
| duration = Chronic | |||
| causes = Unknown, possibly related to [[Epstein-Barr virus]] | |||
| risks = | |||
| diagnosis = Clinical evaluation, [[skin biopsy]] | |||
| differential = [[Varicella]], [[herpes simplex]], [[polymorphous light eruption]] | |||
| prevention = Avoidance of [[sunlight]] | |||
| treatment = [[Sun protection]], [[topical corticosteroids]], [[antiviral therapy]] | |||
| medication = | |||
| prognosis = Generally good, may resolve after adolescence | |||
| frequency = Rare | |||
}} | |||
'''Hydroa Vacciniforme''' is a rare, chronic photodermatosis that primarily affects children and young adults. It is characterized by recurrent vesicles that heal with vacciniform scarring. The condition is often associated with systemic symptoms such as malaise and fever. | '''Hydroa Vacciniforme''' is a rare, chronic photodermatosis that primarily affects children and young adults. It is characterized by recurrent vesicles that heal with vacciniform scarring. The condition is often associated with systemic symptoms such as malaise and fever. | ||
==Etiology== | ==Etiology== | ||
The exact cause of Hydroa Vacciniforme is unknown. However, it is believed to be related to an abnormal response to [[Ultraviolet|UV]] radiation. Some studies have also suggested a possible link with [[Epstein-Barr virus|Epstein-Barr virus (EBV)]] infection. | The exact cause of Hydroa Vacciniforme is unknown. However, it is believed to be related to an abnormal response to [[Ultraviolet|UV]] radiation. Some studies have also suggested a possible link with [[Epstein-Barr virus|Epstein-Barr virus (EBV)]] infection. | ||
==Clinical Presentation== | ==Clinical Presentation== | ||
Patients with Hydroa Vacciniforme typically present with recurrent episodes of vesicles, papules, and crusts on sun-exposed areas. These lesions heal with vacciniform (smallpox vaccine-like) scarring. Systemic symptoms such as malaise and fever may also be present. | Patients with Hydroa Vacciniforme typically present with recurrent episodes of vesicles, papules, and crusts on sun-exposed areas. These lesions heal with vacciniform (smallpox vaccine-like) scarring. Systemic symptoms such as malaise and fever may also be present. | ||
==Diagnosis== | ==Diagnosis== | ||
Diagnosis of Hydroa Vacciniforme is primarily based on clinical findings. [[Dermoscopy|Dermoscopic]] examination may show a characteristic pattern of yellowish-white areas surrounded by a reddish halo. Skin biopsy may reveal changes consistent with a photodermatosis. | Diagnosis of Hydroa Vacciniforme is primarily based on clinical findings. [[Dermoscopy|Dermoscopic]] examination may show a characteristic pattern of yellowish-white areas surrounded by a reddish halo. Skin biopsy may reveal changes consistent with a photodermatosis. | ||
==Treatment== | ==Treatment== | ||
Treatment of Hydroa Vacciniforme is primarily aimed at reducing sun exposure. This can be achieved through the use of sun-protective clothing and broad-spectrum sunscreens. In severe cases, systemic treatments such as [[antimalarial drugs]] or [[immunosuppressive therapy]] may be required. | Treatment of Hydroa Vacciniforme is primarily aimed at reducing sun exposure. This can be achieved through the use of sun-protective clothing and broad-spectrum sunscreens. In severe cases, systemic treatments such as [[antimalarial drugs]] or [[immunosuppressive therapy]] may be required. | ||
==Prognosis== | ==Prognosis== | ||
The prognosis of Hydroa Vacciniforme is generally good, although the condition can be chronic and recurrent. In rare cases, it may progress to a [[lymphoma|cutaneous T-cell lymphoma]]. | The prognosis of Hydroa Vacciniforme is generally good, although the condition can be chronic and recurrent. In rare cases, it may progress to a [[lymphoma|cutaneous T-cell lymphoma]]. | ||
==See Also== | ==See Also== | ||
* [[Photodermatoses]] | * [[Photodermatoses]] | ||
* [[Epstein-Barr virus]] | * [[Epstein-Barr virus]] | ||
* [[Cutaneous T-cell lymphoma]] | * [[Cutaneous T-cell lymphoma]] | ||
[[Category:Dermatology]] | [[Category:Dermatology]] | ||
[[Category:Skin conditions]] | [[Category:Skin conditions]] | ||
[[Category:Rare diseases]] | [[Category:Rare diseases]] | ||
{{stub}} | {{stub}} | ||
Latest revision as of 21:08, 6 April 2025
Editor-In-Chief: Prab R Tumpati, MD
Obesity, Sleep & Internal medicine
Founder, WikiMD Wellnesspedia &
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| Hydroa vacciniforme | |
|---|---|
_Hydroa_vacciniforme.jpg)
| |
| Synonyms | |
| Pronounce | |
| Specialty | Dermatology |
| Symptoms | Vesicular skin lesions, scarring, photosensitivity |
| Complications | N/A |
| Onset | Childhood |
| Duration | Chronic |
| Types | N/A |
| Causes | Unknown, possibly related to Epstein-Barr virus |
| Risks | |
| Diagnosis | Clinical evaluation, skin biopsy |
| Differential diagnosis | Varicella, herpes simplex, polymorphous light eruption |
| Prevention | Avoidance of sunlight |
| Treatment | Sun protection, topical corticosteroids, antiviral therapy |
| Medication | |
| Prognosis | Generally good, may resolve after adolescence |
| Frequency | Rare |
| Deaths | N/A |
Hydroa Vacciniforme is a rare, chronic photodermatosis that primarily affects children and young adults. It is characterized by recurrent vesicles that heal with vacciniform scarring. The condition is often associated with systemic symptoms such as malaise and fever.
Etiology[edit]
The exact cause of Hydroa Vacciniforme is unknown. However, it is believed to be related to an abnormal response to UV radiation. Some studies have also suggested a possible link with Epstein-Barr virus (EBV) infection.
Clinical Presentation[edit]
Patients with Hydroa Vacciniforme typically present with recurrent episodes of vesicles, papules, and crusts on sun-exposed areas. These lesions heal with vacciniform (smallpox vaccine-like) scarring. Systemic symptoms such as malaise and fever may also be present.
Diagnosis[edit]
Diagnosis of Hydroa Vacciniforme is primarily based on clinical findings. Dermoscopic examination may show a characteristic pattern of yellowish-white areas surrounded by a reddish halo. Skin biopsy may reveal changes consistent with a photodermatosis.
Treatment[edit]
Treatment of Hydroa Vacciniforme is primarily aimed at reducing sun exposure. This can be achieved through the use of sun-protective clothing and broad-spectrum sunscreens. In severe cases, systemic treatments such as antimalarial drugs or immunosuppressive therapy may be required.
Prognosis[edit]
The prognosis of Hydroa Vacciniforme is generally good, although the condition can be chronic and recurrent. In rare cases, it may progress to a cutaneous T-cell lymphoma.
