Binder's syndrome

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Binder's Syndrome

Binder's syndrome (pronounced: bin-derz sin-drohm), also known as maxillonasal dysplasia or nasomaxillary hypoplasia, is a rare congenital condition characterized by distinctive facial features, including an underdeveloped upper jaw, a flat nasal bridge, and a short, flat nose.

Etymology

The term "Binder's syndrome" is named after the Austrian physician, Dr. Hermann Binder, who first described the condition in 1962. The term "maxillonasal dysplasia" is derived from the Latin words "maxilla" meaning upper jaw, "nasal" meaning nose, and "dysplasia" meaning abnormal growth or development.

Symptoms

The primary symptoms of Binder's syndrome include a flat, underdeveloped midface, a short, flat nose, and a receding upper jaw. Other symptoms may include malocclusion (improper alignment of the teeth when the jaws are closed), a high-arched palate, and speech difficulties due to the abnormalities in the oral and nasal structures.

Diagnosis

Diagnosis of Binder's syndrome is typically based on a physical examination and the characteristic facial features. Imaging tests such as X-rays or CT scans may be used to confirm the diagnosis and assess the severity of the condition.

Treatment

Treatment for Binder's syndrome is primarily surgical and aims to improve the appearance and function of the face. This may include orthognathic surgery to correct the jaw alignment, rhinoplasty to reshape the nose, and other reconstructive procedures as needed.

Related Terms

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